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姚雪波. Esrp1 and Esrp2 Regulate the Stability of tmc1/2a mRNAs in Zebrafish Sensory Hair Cells. Journal of Neuroscience, 45, 2025.
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闫科吉. EVL is not essential for cuticular plate and stereocilia development in mouse auditory hair cells. FEBS LETTERS, 2025.
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. Mechano-electrical transduction components TMC1-CIB2 undergo a Ca2+-induced conformational change linked to hearing loss. Developmental Cell, 2025.
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Keji Yan, Haoqing Zhang, Chengli Qu, Yuehui Xi, Ze-Guang Han and Zhigang Xu. BAIAP2L1 and BAIAP2L2 differently regulate hair cell stereocilia morphology. FASEB J, 38, 2025.
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Nana Li, Shuang Liu, Dange Zhao, Haibo Du, Yuehui Xi, Xiaoxi Wei, Qingling Liu, Ulrich Müller, Qing Lu, Wei Xiong and Zhigang Xu. Disruption of Cdh23 exon 68 splicing leads to progressive hearing loss in mice by affecting tip-link stability. Proc Natl Acad Sci U S A, 121, e2309656121, 2024.
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Ying Guan, Hai-Bo Du, Zhao Yang, Yu-Zhu Wang, Rui Ren, Wen-Wen Liu, Chao Zhang, Jia-Hai Zhang, Wen-Tao An, Na-Na Li, Xiao-Xue Zeng, Jie Li, Yi-Xiao Sun, Yan-Fei Wang, Fan Yang, Jun Yang, Wei Xiong, Xiao Yu, Ren-Jie Chai, Xiao-Ming Tu, Jin-Peng Sun and Zhi-Gang Xu. Deafness-associated ADGRV1 mutation impairs USH2A stability through improper phosphorylation of WHRN and WDSUB1 recruitment. Advanced Science, 10, e2205993, 2024.
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Xiaoying Wang, Shuang Liu, Qi Cheng, Chengli Qu, Rui Ren, Haibo Du, Nana Li, Keji Yan, Yanfei Wang, Wei Xiong and Zhigang Xu. CIB2 and CIB3 regulate stereocilia maintenance and mechanoelectrical transduction in mouse vestibular hair cells. Journal of Neuroscience, 43, 3219-3231, 2024.
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Rui Ren, Haiyue Xing, Xiaoying Wang, Haibo Du, Yanfei Wang and Zhigang Xu. Loss of TMCC2 activates endoplasm reticulum stress and causes auditory hair cell death. Human Molecular Genetics, 32, 1622-1633, 2024.
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