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孙春娇, 赵静霜, 李娜娜, 姚雪波, 王燕飞, Chul Hoon Kim, Jinwoong Bok, Anthony W. Peng and 徐志刚. Alternative splicing of the Rbm24 gene is essential for cochlear hair cell stereocilia integrity and hearing function in mice. Proc Natl Acad Sci U S A ., 123, e2531564123, 2026.
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宗文, 闫科吉, 邢海月, 张浩晴, 张雯, 高瑞, 彭晓娜, 李唐亮, 汪兆琦 and 徐志刚. Nucleolin is essential for hair cell stereocilia maintenance and auditory function in mice. J Cell Sci, 139, jcs264793, 2026.
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Xuebo Yao, Yan Zhang, Xiaying Hong, Yanyi Xing and Zhigang Xu. Esrp1 and Esrp2 regulate the stability of tmc1/2a mRNAs in zebrafish Sensory Hair Cells. Journal of Neuroscience, 45, e0837242025, 2025.
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Shaoxuan Wu, Lin Lin, Qiaoyu Hu, Xuebo Yao, Hongyang Wang, Shang Liu, Qingling Liu, Yuehui Xi, Yuzhe Lin, Jianqiao Gong, Ruixing Hu, Wei Zhan, Yi Luo, Guang He, Zhijun Liu, Wei Xiong, Qiuju Wang, Zhigang Xu, Fang Bai and Qing Lu. Mechano-electrical transduction components TMC1-CIB2 undergo a Ca2+-induced conformational change linked to hearing loss. Developmental Cell, 60, 1586-1600, 2025.
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Nana Li, Shuang Liu, Dange Zhao, Haibo Du, Yuehui Xi, Xiaoxi Wei, Qingling Liu, Ulrich Müller, Qing Lu, Wei Xiong and Zhigang Xu. Disruption of Cdh23 exon 68 splicing leads to progressive hearing loss in mice by affecting tip-link stability. Proc Natl Acad Sci U S A, 121, e2309656121, 2024.
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Ying Guan, Hai-Bo Du, Zhao Yang, Yu-Zhu Wang, Rui Ren, Wen-Wen Liu, Chao Zhang, Jia-Hai Zhang, Wen-Tao An, Na-Na Li, Xiao-Xue Zeng, Jie Li, Yi-Xiao Sun, Yan-Fei Wang, Fan Yang, Jun Yang, Wei Xiong, Xiao Yu, Ren-Jie Chai, Xiao-Ming Tu, Jin-Peng Sun and Zhi-Gang Xu. Deafness-associated ADGRV1 mutation impairs USH2A stability through improper phosphorylation of WHRN and WDSUB1 recruitment. Advanced Science, 10, e2205993, 2024.
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Xiaoying Wang, Shuang Liu, Qi Cheng, Chengli Qu, Rui Ren, Haibo Du, Nana Li, Keji Yan, Yanfei Wang, Wei Xiong and Zhigang Xu. CIB2 and CIB3 regulate stereocilia maintenance and mechanoelectrical transduction in mouse vestibular hair cells. Journal of Neuroscience, 43, 3219-3231, 2024.
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Rui Ren, Haiyue Xing, Xiaoying Wang, Haibo Du, Yanfei Wang and Zhigang Xu. Loss of TMCC2 activates endoplasm reticulum stress and causes auditory hair cell death. Human Molecular Genetics, 32, 1622-1633, 2024.
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